Abstract
Kronik periaortit daha sık orta yaş erkekleri etkilemekte ve nadir olarak görülmektedir. Patofizyolojisinde
otoimmünitenin etkili olduğu ve idiopatik retroperitoneal fibrozis, perianevrizmal fibrozis, enflamatuar
abdominal aort anevrizması ile ilişkili olduğu ileri sürülmektedir. Retroperitoneal fibrozis olgularının büyük
kısmı idiopatiktir. Mediastinal fibrozis ise sıklıkla enfeksiyoz süreçle ilişkilidir. Bu iki patolojik tablonun
birlikteliği ise oldukça nadirdir. Biz bu çalışmamızda periaortiti olan bir hastamızda eşlik eden
retroperitoneal ve mediastinal fibrozis birlikteliğini sunmayı amaçladık
References
- 1) Comings DE, Skubi KB, Van Eyes J, Motulsky AG. Familial multifocal fibrosclerosis: findings suggesting that retroperitoneal fibrosis, mediastinal fibrosis, sclerosing cholangitis, Riedel's thyroritis, and pseudotumor of the orbit may be different manifestations of a single disease. Ann Intern Med 1967; 166 (5): 884-92. 2) Labidi J, Ariba YB, Chargui S, Bousetta N, Louzir B, Othmani S. Retroperitoneal fibrosis: A retrospective review of clinical presentation, treatment and outcomes. Saudi J Kidney Dis Transpl 2015;26 (4):816-22. 3) Kato T, Minamino E, Nakane E, Miyamoto S,Izumi T, Haruna T, Nohara R, Inoko M. The differential diagnosis of two cases of chronic periaortitis. Case report Radiol. 2013;2013:282067. 4) Vaglio A, Buzio C. Chronic periaortitis: a spectrum of diseases. Curr Opin Rheumatol 2005;17(1):34-40. 5) Zeina AR, Gleb S, Naschitz JE, Loberman Z, Barmeir E. Isolated periaortitis: clinical and imaging characteristics. Vasc Healt Risk Manag 2007;3:1083-6. 6) Vaglio A, Coraddi D, Manenti L et al. Evidence of autoimmunity in chronic periaortitis: a prospective study. Am J Med 2003;114(6):454-62 7) Gilkeson GS, Allen NB: Retroperitoneal fibrosis: a true connective tissue disease. Rheum Dis Clin North Am 1996;22(1): 23-38 8) Light AM. Idiopathic fibrosis of mediastinum: a discussion of three cases and review of the literature. J Clin Pathol 1978;31(1):78-79 9) Cadenas Menendez S, Escudero Bueno C, Gonzalez Budino T. Chylothorax associated with idiopathic mediastinal and retroperitoneal fibrosis. Arch Bronconeumol 2009;45(10):527-8. 10) Cronin CG, Lohan DG, Blake MA, Roche C, McCarthy P, Murphy JM. Retroperitoneal fibrosis: a review of clinical features and imaging findings. AJR Am J Roentgenol 2008;191(2):423-31. 11) Elinav H, Hershko A, Leibovitch G, Naparstek Y. Retroperitoneal fibrosisclinical response to steroid treatment. Harefuah 2003;142(3):166-9
Abstract
Chronic periaortitis is a rare condition. Middle-aged males comprise a large proportion of patients. An
association has been proposed with idiopathic retroperitoneal fibrosis, perianeurysmal fibrosis and
inflammatory abdominal aortic aneurysm, and autoimmunity has been implicated in the pathophysiology.
Comorbidity of retroperitoneal fibrosis, which is frequently idiopathic, and mediastinal fibrosis, which is
particularly associated with infectious processes, is rare. The purpose of this study was to report a case
of comorbid retroperitoneal and mediastinal fibrosis in a patient with periaortitis, together with imaging
findings
References
- 1) Comings DE, Skubi KB, Van Eyes J, Motulsky AG. Familial multifocal fibrosclerosis: findings suggesting that retroperitoneal fibrosis, mediastinal fibrosis, sclerosing cholangitis, Riedel's thyroritis, and pseudotumor of the orbit may be different manifestations of a single disease. Ann Intern Med 1967; 166 (5): 884-92. 2) Labidi J, Ariba YB, Chargui S, Bousetta N, Louzir B, Othmani S. Retroperitoneal fibrosis: A retrospective review of clinical presentation, treatment and outcomes. Saudi J Kidney Dis Transpl 2015;26 (4):816-22. 3) Kato T, Minamino E, Nakane E, Miyamoto S,Izumi T, Haruna T, Nohara R, Inoko M. The differential diagnosis of two cases of chronic periaortitis. Case report Radiol. 2013;2013:282067. 4) Vaglio A, Buzio C. Chronic periaortitis: a spectrum of diseases. Curr Opin Rheumatol 2005;17(1):34-40. 5) Zeina AR, Gleb S, Naschitz JE, Loberman Z, Barmeir E. Isolated periaortitis: clinical and imaging characteristics. Vasc Healt Risk Manag 2007;3:1083-6. 6) Vaglio A, Coraddi D, Manenti L et al. Evidence of autoimmunity in chronic periaortitis: a prospective study. Am J Med 2003;114(6):454-62 7) Gilkeson GS, Allen NB: Retroperitoneal fibrosis: a true connective tissue disease. Rheum Dis Clin North Am 1996;22(1): 23-38 8) Light AM. Idiopathic fibrosis of mediastinum: a discussion of three cases and review of the literature. J Clin Pathol 1978;31(1):78-79 9) Cadenas Menendez S, Escudero Bueno C, Gonzalez Budino T. Chylothorax associated with idiopathic mediastinal and retroperitoneal fibrosis. Arch Bronconeumol 2009;45(10):527-8. 10) Cronin CG, Lohan DG, Blake MA, Roche C, McCarthy P, Murphy JM. Retroperitoneal fibrosis: a review of clinical features and imaging findings. AJR Am J Roentgenol 2008;191(2):423-31. 11) Elinav H, Hershko A, Leibovitch G, Naparstek Y. Retroperitoneal fibrosisclinical response to steroid treatment. Harefuah 2003;142(3):166-9
Details
| Primary Language | English |
|---|---|
| Journal Section | Case Report |
| Authors | |
| Publication Date | April 28, 2017 |
| Submission Date | December 19, 2016 |
| Published in Issue | Year 2017 Volume: 14 Issue: 1 |
Harran Üniversitesi Tıp Fakültesi Dergisi / Journal of Harran University Medical Faculty