Anesthetic Management of An Obstetric Patient With Limb-Girdle Muscular Dystrophy: Case Report and Review of The Literature
Abstract
Limb-girdle muscular dystrophy is a rare hereditary disease with dangerous systemic components including difficult airway, muscle weakness, increased risk for pulmonary aspiration, cardiomyopathy, and rhabdomyolysis that make anesthetic management challenging. In this case report, we aimed to discuss the anesthetic management of a 36-year-old pregnant woman with Limb-Girdle Muscular Dystrophy LGMD who underwent emergent caesarean section with spinal anesthesia and to review of the anesthetic management of obstetric Limb-Girdle patients in the literature
References
- Bushby KM, Beckmann JS. The limb-girdle muscular dystrophies - Proposal for a new nomenclature. Neuromuscul Disord 1995;5:337– 43. [CrossRef]
- Allen T, Maguire S. Anaesthetic management of a woman with autosomal recessive limb-girdle muscular dystrophy for emergency caesarean section. Int J Obstet Anesth 2007;16:370–4. [CrossRef]
- Van der Kooi AJ, Barth PG, Busch HF, de Haan R, Ginjaar HB, van Essen AJ, et al. The clinical spectrum of limb girdle muscular dystrophy. A survey in the Netherlands. Brain 1996;119:1471–80. [CrossRef]
- Driessen JJ. Neuromuscular and mitochondrial disorders: what is relevant to the anaesthesiologist? Curr Opin Anaesthesiol 2008;21:350–5. [CrossRef]
- Sarkılar G, Mermer A, Yücekul M, Ceken BM, Altun C, Otelcioglu S. Anaesthetic management of a child with limb-girdle muscular dystrophy. Turk J Anaesth Reanim 2014;42:103–5. [CrossRef]
- Ranjan RV, Ramachandran TR, Manikandan S, John R. Limb-girdle muscular dystrophy with obesity for elective cesarean section: Anesthetic management and brief review of the literature. Anesth Essays Res 2015;9:127–9. [CrossRef]
- Duggan M, Kavanaugh B P. Pulmonary Atelectasis: A pathogenic perioperative entity. Anesthesiology 2005;102:838–54. [CrossRef]
- Yılmaz R, Reisli R, Tosun OM, Topal A, Uzun ST. Anesthetic Management of a Pregnant Woman with Limb-Girdle Muscular Dystrophy. JARSS 2019;27:70–3. [CrossRef]
- Pash PM, Balaton J, Eagle C. Anaesthetic management of a parturient with severe muscular dystrophy, lumbar lordosis and a difficult airway. Can J Anesth 1996;43:959–63. [CrossRef]
LIMB-GIRDLE MUSKÜLER DISTROFILI OBSTETRIK HASTADA ANESTEZI YÖNETIMI: VAKA TAKDIMI VE LITERATÜR TARAMASI
Abstract
Limb-girdle musküler distrofi zor havayolu, kas zayıflığı, artmış pulmoner aspirasyon riski, kardiomyopati ve rabdomyoliz gibi tehlikeli sistemik komponentleri olan, genetik geçişli, seyrek görülen bir hastalıktır. Bu vakada, Limb girdle musküler distrofili 36 yaşında bir gebenin spinal anestezi ile acil sezaryeni sırasındaki anestezi yönetimini ve literatürdeki obstetrik Limb-girdle musküler distrofi hastalarını gözden geçirmeyi amaçladık
References
- Bushby KM, Beckmann JS. The limb-girdle muscular dystrophies - Proposal for a new nomenclature. Neuromuscul Disord 1995;5:337– 43. [CrossRef]
- Allen T, Maguire S. Anaesthetic management of a woman with autosomal recessive limb-girdle muscular dystrophy for emergency caesarean section. Int J Obstet Anesth 2007;16:370–4. [CrossRef]
- Van der Kooi AJ, Barth PG, Busch HF, de Haan R, Ginjaar HB, van Essen AJ, et al. The clinical spectrum of limb girdle muscular dystrophy. A survey in the Netherlands. Brain 1996;119:1471–80. [CrossRef]
- Driessen JJ. Neuromuscular and mitochondrial disorders: what is relevant to the anaesthesiologist? Curr Opin Anaesthesiol 2008;21:350–5. [CrossRef]
- Sarkılar G, Mermer A, Yücekul M, Ceken BM, Altun C, Otelcioglu S. Anaesthetic management of a child with limb-girdle muscular dystrophy. Turk J Anaesth Reanim 2014;42:103–5. [CrossRef]
- Ranjan RV, Ramachandran TR, Manikandan S, John R. Limb-girdle muscular dystrophy with obesity for elective cesarean section: Anesthetic management and brief review of the literature. Anesth Essays Res 2015;9:127–9. [CrossRef]
- Duggan M, Kavanaugh B P. Pulmonary Atelectasis: A pathogenic perioperative entity. Anesthesiology 2005;102:838–54. [CrossRef]
- Yılmaz R, Reisli R, Tosun OM, Topal A, Uzun ST. Anesthetic Management of a Pregnant Woman with Limb-Girdle Muscular Dystrophy. JARSS 2019;27:70–3. [CrossRef]
- Pash PM, Balaton J, Eagle C. Anaesthetic management of a parturient with severe muscular dystrophy, lumbar lordosis and a difficult airway. Can J Anesth 1996;43:959–63. [CrossRef]
Details
| Primary Language | English |
|---|---|
| Journal Section | Research Article |
| Authors | |
| Publication Date | December 1, 2020 |
| Published in Issue | Year 2020Issue: 4 |