Abstract
Clear cell sarcoma is a very rare tumor that is intimately associated with tendons and aponeuroses. Females are affected more commonly than males, and the patients are usually between 20 and 40 years of age. The typical sites for clear cell sarcoma are the limbs, especially the foot and ankle region. It is a highly malignant tumor that usually requires wide or radical excision. A case of a clear cell sarcoma in the anteromedial aspect of the left foot of a 52-yearold woman is described. Clinical and radiologic presentation and histologic evaluation of clear cell sarcoma is discussed, in order to make a differential diagnosis between this rare tumor and other soft tissue tumors. In addition, the treatment principles of the tumor are identified. This case demonstrates that clear cell sarcoma can be difficult to diagnose without histologic evaluation and, once diagnosed, should be treated by adequate surgical excision in order to prevent recurrence and distant metastases
Keywords
References
- Reichert B, Hoch J, Plotz W, Mailander P, Moubayed P. Metastatic clear-cell sarcoma of the capitate. Olgu raporu. J Bone Joint Surg Am. 2001;83- A(11):1713-7.
- Enzinger FM, Wiess SW. Benign lipoblastoma and lipoblastomatosis. In Enzinger FM, Wiess SW (eds). Soft tissue tumors. Ed 3th. St. Louis, CV Mosby. 601-605.
- Morishita S, Onomura T, Yamamoto S, Nakashima Y. Clear cell sarcoma of tendons and aponeuroses (malignant melanoma of soft parts) with unusual roentgenologic findings. Olgu raporu. ClinOrthop. 1987;216:276-9.
- Seale KS, Lange TA, Monson D, Hackbarth DA. Soft tissue tumors of the foot and ankle. Foot Ankle. 1988 Aug;9(1):19-27.
- Hazra S, Weiner SD, Senior ME, Seth A. Painless enlarging subcutaneous mass in a 58-year-old woman. Klinik Ortpedi. 2000 ;(370):311-4, 317-9.
- Gelczer RK, Wenger DE, Wold LE. Primary clear cell sarcoma of bone: a unique site of origin. Skeletal Radiol. 1999;28(4):240-3.
- Canale ST. Soft tissue tumors. In Canale ST. Campbell’s operative orthopaedics. Ed 9 th Memphis,Tennesse, Mosby.742-766.
- Shives TC. Biopsy of soft-tissue tumors. Klinik Ortopedi. 1993 Apr;(289):32-5.
- Deenik W, Mooi WJ, Rutgers EJ, Peterse JL, Hart AA, Kroon BB. Clear cell sarcoma (malignant melanoma) of soft parts: A clinicopathologic study of 30 cases. Cancer. 1999 Eylül 15;86(6):969-75.
- Ferrari A, Casanova M, Bisogno G, Mattke A, Meazza C, Gandola L, Sotti G, Cecchetto G, Harms D, Koscielniak E, Treuner J, Carli M. Clear cell sarcoma of tendons and aponeuroses in pediatric patients: a report from the Italian and German. Soft Tissue Sarcoma Cooperative Group. Cancer. 2002 Haziran 15;94(12):3269-76.
Abstract
Şeffaf hücreli sarkom tendon ve aponevrozlarla sıkı şekilde ilişkili olan nadir bir tümördür. Kadınlarda erkeklere göre daha sık rastlanılır ve hastalar genelde 20 ile 40 yaş arasındadır. Şeffaf hücreli sarkom tipik olarak ekstremiteleri tutar. Ayak ve ayak bileği sık olarak tutulan bölgelerdir. Ayrıca yüksek derecede agresif bir tümördür ve genelde geniş yada radikal cerrahi ile çıkarılması gerekir. 52 yaşındaki bayan hastanın sol ayağının anteromediyalinde Şeffaf hücreli sarkom tespit edilmiştir. Bu nadir tümör ile diğer yumuşak doku tümörlerinin ayırıcı tanısını yapmak için; Şeffaf hücre sarkomunun klinik durumu, radyolojik görünümü ve histolojik değerlendirmesi yapıldı. Ayrıca, tümörün tedavi ilkeleri tanımlandı. Bu vaka Şeffaf hücreli karsinoma histolojik değerlendirme olmadan tanı koymanın zor olduğunu ve bir kez tanı konduğu zaman tümörün yeniden ortaya çıkmasını ve metastazını engellemek için yeterli cerrahi eksizyon ile tedavi edilmesi gerektiğini göstermektedir
Keywords
References
- Reichert B, Hoch J, Plotz W, Mailander P, Moubayed P. Metastatic clear-cell sarcoma of the capitate. Olgu raporu. J Bone Joint Surg Am. 2001;83- A(11):1713-7.
- Enzinger FM, Wiess SW. Benign lipoblastoma and lipoblastomatosis. In Enzinger FM, Wiess SW (eds). Soft tissue tumors. Ed 3th. St. Louis, CV Mosby. 601-605.
- Morishita S, Onomura T, Yamamoto S, Nakashima Y. Clear cell sarcoma of tendons and aponeuroses (malignant melanoma of soft parts) with unusual roentgenologic findings. Olgu raporu. ClinOrthop. 1987;216:276-9.
- Seale KS, Lange TA, Monson D, Hackbarth DA. Soft tissue tumors of the foot and ankle. Foot Ankle. 1988 Aug;9(1):19-27.
- Hazra S, Weiner SD, Senior ME, Seth A. Painless enlarging subcutaneous mass in a 58-year-old woman. Klinik Ortpedi. 2000 ;(370):311-4, 317-9.
- Gelczer RK, Wenger DE, Wold LE. Primary clear cell sarcoma of bone: a unique site of origin. Skeletal Radiol. 1999;28(4):240-3.
- Canale ST. Soft tissue tumors. In Canale ST. Campbell’s operative orthopaedics. Ed 9 th Memphis,Tennesse, Mosby.742-766.
- Shives TC. Biopsy of soft-tissue tumors. Klinik Ortopedi. 1993 Apr;(289):32-5.
- Deenik W, Mooi WJ, Rutgers EJ, Peterse JL, Hart AA, Kroon BB. Clear cell sarcoma (malignant melanoma) of soft parts: A clinicopathologic study of 30 cases. Cancer. 1999 Eylül 15;86(6):969-75.
- Ferrari A, Casanova M, Bisogno G, Mattke A, Meazza C, Gandola L, Sotti G, Cecchetto G, Harms D, Koscielniak E, Treuner J, Carli M. Clear cell sarcoma of tendons and aponeuroses in pediatric patients: a report from the Italian and German. Soft Tissue Sarcoma Cooperative Group. Cancer. 2002 Haziran 15;94(12):3269-76.
Details
| Primary Language | Turkish |
|---|---|
| Journal Section | Research Article |
| Authors | |
| Publication Date | June 1, 2010 |
| Published in Issue | Year 2010Issue: 2 |