Öz
Cor-triatriatum sinister is a rare congenital heart defect that is characterised by the division of left atrium by a fibromuscular membrane into two seperate chambers. It is a rare congenital defect first reported by Church in 1868 1 . It is extremely rare, with an incidence of 0.1-0.4 %, during pediatric age. Its appearence in adulthood is even more exceptional and often incidentally discovered 2 . Classically, patients present during the neonatal period or early infancy although in some cases remain undetected until the patient is an adult. We report an unusual case of cor traitriatum sinister in an 73-year old woman which was concidentally discovered during preoperative evaluation
Anahtar Kelimeler
Kaynakça
- Church WS. Congenital malformation of the heart: abnormal septum in the left auricle. Trans Pathol Soc Lond 1868;19:188–90.
- Almendro-Delia M, Trujillo-Berraquero F, Araji O, de Vinuesa PG, Fernández JM. Cor triatriatum sinistrum in an elderly man.Int J Cardiol. 2008 Apr 10;125(2):e27-9. Epub 2007 Oct 18.
- Akintunde AA.Cor triatriatum in an 86-year-old woman: initial presentation with pulmonary hypertension discovered during preoperative evaluation.Singapore Med J. 2011 Oct;52(10):e203-5.
- Chen Q, Guhathakurta S, Vadalapali G, Nalladaru Z, Easthope RN, Sharma AK.Cor triatriatum in adults: three new cases and a brief review.Tex Heart Inst J. 1999;26(3):206-10. Review.
- Loeffler E.Unusual malformation of the left atrium; pulmonary sinus. Arch Pathol (Chic). 1949 Nov;48(5):371-6.
Öz
Cor triatriatum sinister oldukça nadir görülen bir konjenital kalp hastalığı olup sol atriumun, fibromüsküler membran ile iki faklı bölmeye ayrılması ile karakterizedir. İlk olarak 1868’de Church tarafından rapor edilmiştir 1 . Oldukça nadir olarak gözlenen bu kardiyak anomalinin insidansı pediatrik yaş grubunda %0.1-0.4’tür. Erişkinlerde çok daha nadir olarak görülmekte olan cor triatriatumun tanısı ise sıklıkla rastantısal olarak konulmaktadır 2 . Klasik olarak, hastalara neonatal dönemde veya erken infant döneminde tanı konulsa da bazı vakalar erişkin döneme kadar saptanamayabilmektedir. Vaka sunumumuzda, koroner arter hastalığı nedeniyle cerrahi planlanan ve preoperatif incelemede rastlantısal olarak cor triatritum sinister saptanan 73 yaşındaki kadın hastadan bahsedilmiştir
Anahtar Kelimeler
Kaynakça
- Church WS. Congenital malformation of the heart: abnormal septum in the left auricle. Trans Pathol Soc Lond 1868;19:188–90.
- Almendro-Delia M, Trujillo-Berraquero F, Araji O, de Vinuesa PG, Fernández JM. Cor triatriatum sinistrum in an elderly man.Int J Cardiol. 2008 Apr 10;125(2):e27-9. Epub 2007 Oct 18.
- Akintunde AA.Cor triatriatum in an 86-year-old woman: initial presentation with pulmonary hypertension discovered during preoperative evaluation.Singapore Med J. 2011 Oct;52(10):e203-5.
- Chen Q, Guhathakurta S, Vadalapali G, Nalladaru Z, Easthope RN, Sharma AK.Cor triatriatum in adults: three new cases and a brief review.Tex Heart Inst J. 1999;26(3):206-10. Review.
- Loeffler E.Unusual malformation of the left atrium; pulmonary sinus. Arch Pathol (Chic). 1949 Nov;48(5):371-6.
Ayrıntılar
| Birincil Dil | Türkçe |
|---|---|
| Bölüm | Case Report |
| Yazarlar | |
| Yayımlanma Tarihi | 1 Haziran 2013 |
| Yayımlandığı Sayı | Yıl 2013Sayı: 2 |