Anesthetic Management of a Pediatric Patient With Larsen Syndrome

Number: 4 December 1, 2016
  • Mahmut Alp Karahan
  • Nuray Altay
  • Hasan Hüsnü Yüce
  • Mehmet Eroğlu
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Anesthetic Management of a Pediatric Patient With Larsen Syndrome

Abstract

Larsen syndrome is a rare, inherited, connective tissue disorder which is characterized by facial dysmorphisms, congenital joint dislocations and multi-system involvement including musculoskeletal, respiratory, cardiovascular, and neurological systems. Children with Larsen syndrome are prone to undergo a wide variety of surgical treatments for their orthopedic abnormalities. For this reason these patients may require repeated anesthetic care during surgical procedures. The major concerns about these patients regarding anesthesia include perioperative respiratory dysfunction, cardiovascular problems and difficult airway management. Laryngomalacia, tracheomalacia, bronchomalacia and subglottic stenosis are the main causes for difficult airway management in this syndrome. In this case report we discussed, in light of literature, the anesthetic management of a pediatric patient with Larsen syndrome who underwent a pes equinovarus surgery

Keywords

References

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Details

Primary Language

Turkish

Subjects

-

Journal Section

-

Authors

Mahmut Alp Karahan

Nuray Altay

Hasan Hüsnü Yüce

Mehmet Eroğlu

Publication Date

December 1, 2016

Submission Date

-

Acceptance Date

-

Published in Issue

Year 1970 Number: 4

IZ

https://izlik.org/JA76ER34MH

Cite

RIS / Bibtex
EndNote
Karahan MA, Altay N, Yüce HH, Eroğlu M (December 1, 2016) Larsen Sendromlu Pediatrik Hastada Anestezi Yönetimi. Acıbadem Üniversitesi Sağlık Bilimleri Dergisi 4 230–233.