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Management of a Neonate with a Rare Congenital Palatosubglossal Synechia in Pierre Robin Sequence

Year 2015, Issue: 4, 223 - 225, 01.12.2015

Abstract

Development of the human face begins in the fourth week of gestation, as a series of several complicated and well-organized sequential intrauterine events, disruption of which causes some sort of facial dismorhogenesis. Oral synechiae is a rare congenital anomaly usually recognized at birth secondary to airway or nutritional compromise. They help to understand the intrauterine developmental steps of the facial region. In this particular case with congenital palatosubglossal synechia, anterior soft palate of the patient with Pierre Robin sequence was repaired with the oral mucosal flap elevated from the floor of the mouth by using the synechial band as the pedicle of the flap

References

  • Tepper OM, Warren SM. Craniofacial Embryology. In: Weinzweig J. eds Plastic Surgery Secrets. Philadelphia: Mosby Elsevier, 2010:139-45
  • Moore KL. The Developing Human,3rdedn. WB Saunders, Philadelphia, PA, 1988: 197–213.
  • Sunder RA, Manikandan R, Kumar M. Airway management of a neonate with a rare congenital palatoglossalsynechiae. Pediatric Anesthesia 2008; 18: 976–1014.
  • Laster Z, Temkin D, Zarfin Y et al. A complete bony fusion of the mandible to the zygomatic complex and maxillary tuberosity: case report end review. Int J Oral Maxillofac Surg 2001;30:75–9.
  • Smith DM, Vecchione L, Jiang S, Ford M, Deleyiannis FW, Haralam MA, et al. The Pittsburgh Fistula Classification System: a standardized scheme for the description of palatal fistulas. Cleft Palate Craniofac J. 2007;44:590-4.

PİERRE ROBİN SENDROMLU BİR YENİDOĞANDA NADİR GÖRÜLEN PALATOSUBGLOSAL YAPIŞIKLIĞIN TEDAVİSİ

Year 2015, Issue: 4, 223 - 225, 01.12.2015

Abstract

Yüzün gelişimi hamileliğin 4. haftasında başlar. İyi organize, bazı komplike intrauterin olayların ardısıra cerayan etmesi sonucu yüzün gelişimi tamamlanır. Bu süreçleri bozacak olaylar ise çeşitli fasiyal dismorfogenetik olaylara neden olabilir. Ağız içinde sineşi görülmesi nadir bir konjenital durumdur. Genelde doğum sonrasında nefes problemleri ve beslenme problemlerine neden olabileceği için tanı konulur. Bu gelişimsel bozukluklar bize yüzün embriyoljik olarak nasıl geliştiği konusunda da ip ucu verir. Bu vaka sunumumuzda Pierre Robin Sekanslı bir hastada olan palatosubglossal sineşi bandının pedikül olarak kullanılarak, dilin alt tarafından kaldırılan mukoza flebi ile onarılan anterior palatal yarığın tedavisini sunduk.

References

  • Tepper OM, Warren SM. Craniofacial Embryology. In: Weinzweig J. eds Plastic Surgery Secrets. Philadelphia: Mosby Elsevier, 2010:139-45
  • Moore KL. The Developing Human,3rdedn. WB Saunders, Philadelphia, PA, 1988: 197–213.
  • Sunder RA, Manikandan R, Kumar M. Airway management of a neonate with a rare congenital palatoglossalsynechiae. Pediatric Anesthesia 2008; 18: 976–1014.
  • Laster Z, Temkin D, Zarfin Y et al. A complete bony fusion of the mandible to the zygomatic complex and maxillary tuberosity: case report end review. Int J Oral Maxillofac Surg 2001;30:75–9.
  • Smith DM, Vecchione L, Jiang S, Ford M, Deleyiannis FW, Haralam MA, et al. The Pittsburgh Fistula Classification System: a standardized scheme for the description of palatal fistulas. Cleft Palate Craniofac J. 2007;44:590-4.
There are 5 citations in total.

Details

Primary Language Turkish
Journal Section Case Report
Authors

Kahraman Berkhan Yılmaz

Halil İbrahim Canter

Mustafa Engin Çakmakçı

Publication Date December 1, 2015
Published in Issue Year 2015Issue: 4

Cite

EndNote Yılmaz KB, Canter Hİ, Çakmakçı ME (December 1, 2015) PİERRE ROBİN SENDROMLU BİR YENİDOĞANDA NADİR GÖRÜLEN PALATOSUBGLOSAL YAPIŞIKLIĞIN TEDAVİSİ. Acıbadem Üniversitesi Sağlık Bilimleri Dergisi 4 223–225.