Konjenital Skolyoz Tanı ve Tedavisi

Çağlar Yılgör; İrem Nur Eroğlu; Nuray Söğünmez; Kadir Abul; Ahmet Alanay

EN TR

Konjenital Skolyoz Tanı ve Tedavisi

Öz

Omurganın en sık görülen konjenital deformitesi konjenital skolyozdur. Deformiteyi oluşturan sebep, oluşum veya ayrışma kusuru veya bu iki bozukluğun birlikte olduğu karma tiptir. Kliniğe yansıması, stabil hemivertebradan, pulmoner, kardiyak, genitoüriner ve nörolojik komplikasyonlara yol açabilen karmaşık ve ilerleyici deformitelere kadar geniş bir aralıktadır. Tabloya sıklıkla diğer organ sistemlerindeki anomaliler eşlik eder. Tanıda; prenatal ultrason, fizik muayene ve röntgen kullanılır. Manyetik rezonans eşlik eden intradural patolojilerin ortaya konulmasında yardımcıdır. Bilgisayarlı tomografi cerrahi planlamada yardımcı olabilir. Tedavi planı eğriliğin yeri ve derecesi, hastanın yaşı, deformitenin tipine ve öngörülen ilerleme beklentisine göre her hastaya özel olarak yapılır. Tedavi temel olarak kontrollü gözlem, konservatif ve cerrahi tedavilerden oluşur. Tek hemivertebra varlığında genellikle erken yaşta hemivertebrektomi ve limitli füzyon önerilir. Daha karmaşık deformitelerde hemiepifizyodez, distraksiyon temelli füzyonsuz cerrahi yöntemler veya bunların kombinasyonları kullanılabilir. Günümüzde teknolojik ilerlemeler sayesinde spinal deformite ve intradural patolojilerin cerrahisi eş zamanlı olarak güvenli şekilde yapılabilmektedir. İhmal edilmiş ileri deformitelerde düzeltici osteotomiler gerekebilir. Düzeltici osteotomiler barındırdıkları nörolojik yaralanma riski ve uygulamadaki teknik zorluklar nedeniyle donanımlı merkezlerde deneyimli cerrahlar tarafından gerçekleştirilmelidir

Anahtar Kelimeler

Omurga,doğumsal anomaliler,skolyoz,kifoz,hemivertebra

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Turkish

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-

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Çağlar Yılgör

İrem Nur Eroğlu

Nuray Söğünmez

Kadir Abul

Ahmet Alanay

Publication Date

June 1, 2019

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Published in Issue

Year 2019 Number: 2

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https://izlik.org/JA64ED26NN

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Yılgör Ç, Eroğlu İN, Söğünmez N, Abul K, Alanay A (June 1, 2019) Konjenital Skolyoz Tanı ve Tedavisi. Acıbadem Üniversitesi Sağlık Bilimleri Dergisi 2 148–155.

Konjenital Skolyoz Tanı ve Tedavisi

Diagnosis and Treatment of Congenital Scoliosis

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Konjenital Skolyoz Tanı ve Tedavisi

Öz

Anahtar Kelimeler

References

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