Anesthetic Management of Scoliosis Surgery For a Patient With Joubert Syndrome: a Case Report

Number: 1 March 1, 2019
  • Mehmet Bilhan Hayırlıoğlu
  • Banu Gökay Vural
  • Müzeyyen İyigün
  • Tayfun Güler
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Acıbadem Üniversitesi Sağlık Bilimleri Dergisi
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Anesthetic Management of Scoliosis Surgery For a Patient With Joubert Syndrome: a Case Report

Abstract

Joubert Syndrome is a rare, autosomal recessive AR disorder characterized byneurologic findings as hypotonia, ataxia, physhcomotor developmental delay, abnormal respiratory pattern and abnormal eye movements. Molar tooth sign caused by cerebellar vermis hypoplasia is a neuroradiologic diagnostic criteria in cranial magnetic resonance imaging MRI . Scolisosis is common in these patients due to hypotonia during the early developmental period. In this article we presented our anesthesia management during scoliosis correction surgery in a patient with Joubert Syndrome

Keywords

References

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  7. Yang J, Huang Z, Shu H, Chen Y, Sun X, Liu W, et al. Improving successful rate of transcranial electrical motor-evoked potentials monitoring during spinal surgery in young children. Eur Spine J 2012;21:980–4. [CrossRef]
  8. Glover DC, Carling PN. Neuromonitoring for Scoliosis Surgery. Anesthesiology Clin 2014;32:101–14. [CrossRef]

Details

Primary Language

Turkish

Subjects

-

Journal Section

-

Authors

Mehmet Bilhan Hayırlıoğlu

Banu Gökay Vural

Müzeyyen İyigün

Tayfun Güler

Publication Date

March 1, 2019

Submission Date

-

Acceptance Date

-

Published in Issue

Year 1970 Number: 1

IZ

https://izlik.org/JA35RU94DR

Cite

RIS / Bibtex
EndNote
Hayırlıoğlu MB, Vural BG, İyigün M, Güler T (March 1, 2019) Joubert Sendromlu Hastanın Skolyoz Cerrahisinde Anestezi Yönetimi: Olgu Sunumu. Acıbadem Üniversitesi Sağlık Bilimleri Dergisi 1 110–112.